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Overview

Uniprot IDA0A8I5ZKU7
Protein NameIsovaleryl-CoA dehydrogenase, mitochondrial
Gene NameIvd
OrganismRattus norvegicus

Kla Sites from experimental identification

Position Flanking peptide
56 QLRHTISKFVQENLA
76 IDQSNDFKNLREFWK

Function

A mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism, where isovaleryl-CoA (3-methylbutanoyl-CoA) is metabolized to 3-methylbut-2-enoyl-CoA. To a lesser extent, it also participates in the first step in fatty acid beta-oxidation, in which it catalyzes the proR-proR stereospecific alpha,beta-dehydrogenation of other saturated short-chain acyl-CoA thioesters such as pentanoyl-CoA, hexanoyl-CoA and butanoyl-CoA, using the electron transfer flavoprotein (ETF) as their physiologic electron acceptor

Protein Sequence

10 MATAVRLLGR 20 RVSSWRLRPL 30 PSPLAVPQRA 40 HSMLPVDDDI 50 NGLNEEQKQL 60 RHTISKFVQE 70 NLAPKAQEID 80 QSNDFKNLRE 90 FWKQLGSLGV 100 LGITAPVQYG 110 GSGLGYLEHV 120 LVMEEISRAS 130 AAVGLSYGAH 140 SNLCINQIVR 150 NGNEAQKEKY 160 LPKLISGEFI 170 GALAMSEPNA 180 GSDVVSMRLK 190 AEKKGDHYVL 200 NGNKFWITNG 210 PDADVLVVYA 220 KTDLTAVPAS 230 RGITAFIVEK 240 VSVVGPLTSV 250 YPAAANILSQ 260 ESKGVYVLMS 270 GLDLERLVLA 280 GGPLGIMQAV 290 LDHTIPYLHV 300 REAFGQKIGQ 310 FQLMQGKMAD 320 MYTRLMACRQ 330 YVYNVARACD 340 EGHITAKDCA 350 GVILYTAECA 360 TQVALDGIQC 370 LGGNGYINDF 380 PMGRFLRDAK 390 LYEIGGGTSE 400 VRRLVIGRAF NADFR

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0008470 3-methylbutanoyl-CoA dehydrogenase activity
Molecular Function GO:0050660 flavin adenine dinucleotide binding
Biological Process GO:0046395 carboxylic acid catabolic process

Reference

[1] Chen Y, Sun W, Sun Z, Zhao H, Wu T et al.. Effect of electroacupuncture on hippocampal protein lactylation in a rat model of vascular dementia.. Front Neurol 16:1629474. 2025. PMID: 40963935.