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Overview

Uniprot IDA0A8I5ZQL5
Protein NameIsobutyryl-CoA dehydrogenase, mitochondrial
Gene NameAcad8
OrganismRattus norvegicus

Kla Sites from experimental identification

Position Flanking peptide
211 RTGGSGPKGISCIVV

Function

Isobutyryl-CoA dehydrogenase which catalyzes the conversion of 2-methylpropanoyl-CoA to (2E)-2-methylpropenoyl-CoA in the valine catabolic pathway. To a lesser extent, also able to catalyze the oxidation of (2S)-2-methylbutanoyl-CoA

Protein Sequence

10 VAMLRTGSRR 20 LGCLRAALQS 30 LAQTDHRSIT 40 FCIDPSLGLN 50 EEQKGFQKVA 60 FDFAAREMAP 70 NMAEWDQKEL 80 FPVDVMRKAA 90 QLGFGGIYVR 100 TDVGGSGLSR 110 LDTSVIFEAL 120 ATGCTSTTAY 130 ISIHNMCAWM 140 IDSFGNEEQR 150 HKFCPPLCTM 160 EKFASYCLTE 170 PGSGSDAASL 180 LTSAKRQGDH 190 YILNGSKAFI 200 SGGGESDIYV 210 VMCRTGGSGP 220 KGISCIVVEK 230 GTPGLSFGKK 240 EKKVGWNSQP 250 TRAVIFEDCA 260 VPVANRIGTE 270 GQGFLIAMKG 280 LNGGRINVAS 290 CSLGAAHASV 300 VLTQEHLKVR 310 KQFGAPLARS 320 QYLQFQLADM 330 ATKLVASRLM 340 IRTAAVALQE 350 EREDAVALCS 360 MAKLFVTEEC 370 FTICNQALQM 380 HGGYGYLKDY 390 AVQQYMRDSR 400 VHQILEGSNE 410 VMRMLISRSL LQD

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0050660 flavin adenine dinucleotide binding
Molecular Function GO:0003853 short-chain 2-methyl fatty acyl-CoA dehydrogenase activity
Biological Process GO:0009083 branched-chain amino acid catabolic process
Biological Process GO:0006635 fatty acid beta-oxidation

Reference

[1] Chen Y, Sun W, Sun Z, Zhao H, Wu T et al.. Effect of electroacupuncture on hippocampal protein lactylation in a rat model of vascular dementia.. Front Neurol 16:1629474. 2025. PMID: 40963935.