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Overview

Uniprot IDD3ZKG1
Protein NameMethylmalonyl-CoA mutase, mitochondrial
Gene NameMmut
OrganismRattus norvegicus

Kla Sites from experimental identification

Position Flanking peptide
685 KEITSAIKRVNKFME

Function

Catalyzes the reversible isomerization of methylmalonyl-CoA (MMCoA) (generated from branched-chain amino acid metabolism and degradation of dietary odd chain fatty acids and cholesterol) to succinyl-CoA (3-carboxypropionyl-CoA), a key intermediate of the tricarboxylic acid cycle

Protein Sequence

10 MKKPDTLVEK 20 GWTKGVCLIR 30 HQTRARNGGI 40 GLAEPRAELA 50 TPPELTGSGA 60 PAASASGSRA 70 LGFDLRGRPP 80 TLFVLIFVWE 90 YSCFTMLRAK 100 NQLFLLSPHY 110 LKQLKDASSY 120 RWKRLLHQQQ 130 PLHPEWAVLA 140 KKQLKGKNPE 150 DLIWHTPEGI 160 SIKPLYSRAD 170 TMDLPEELPG 180 VKPFTRGPYP 190 TMYTYRPWTI 200 RQYAGFSTVE 210 ESNKFYKDNI 220 KAGQQGLSVA 230 FDLATHRGYD 240 SDNPRVRGDV 250 GMAGVAIDTV 260 EDTKILFDGI 270 PLEKMSVSMT 280 MNGAVIPVLA 290 TFIVTGEEQG 300 VPKEKLTGTI 310 QNDILKEFMV 320 RNTYIFPPEP 330 SMKIIADIFQ 340 YTAQHMPKFN 350 SISISGYHMQ 360 EAGADAILEL 370 AYTIADGLEY 380 CRTGLQAGLT 390 IDEFAPRLSF 400 FWGIGMNFYM 410 EIAKMRAGRR 420 LWAHLIEKMF 430 QPKNSKSLLL 440 RAHCQTSGWS 450 LTEQDPYNNI 460 VRTAIEAMAA 470 VFGGTQSLHT 480 NSFDEALGLP 490 TVKSARIARN 500 TQIIIQEESG 510 IPKVADPWGG 520 SYMMESLTND 530 VYEAALKLIY 540 EVEEMGGMAK 550 AVAEGIPKLR 560 IEECAARRQA 570 RIDSGSEVIV 580 GVNKYQLEKE 590 DSVEVLAIDN 600 TSVRKKQIEK 610 LKKIKSSRDQ 620 ALAERSLNAL 630 TQCAASGDGN 640 ILALAVDAAR 650 ARCTVGEITD 660 ALKKVFGEHK 670 ANDRMVSGAY 680 RQEFGESKEI 690 TSAIKRVNKF 700 MEREGRRPRL 710 LVAKMGQDGH 720 DRGAKVIATG 730 FADLGFDVDI 740 GPLFQTPREV 750 AQQAVDADVH 760 AVGVSTLAAG 770 HKTLVPELIK 780 ELSALGRPDI 790 LVMCGGVIPP 800 QDYEFLYEVG 810 VSNVFGPGTR 820 IPKAAVQVLD 830 DIEKSLAEKQ QSV

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005737 cytoplasm
Cellular Component GO:0005759 mitochondrial matrix
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0031419 cobalamin binding
Molecular Function GO:0003924 GTPase activity
Molecular Function GO:0042802 identical protein binding
Molecular Function GO:0046872 metal ion binding
Molecular Function GO:0004494 methylmalonyl-CoA mutase activity
Molecular Function GO:0072341 modified amino acid binding
Molecular Function GO:0042803 protein homodimerization activity
Biological Process GO:0050667 homocysteine metabolic process
Biological Process GO:0043547 positive regulation of GTPase activity
Biological Process GO:0009791 post-embryonic development
Biological Process GO:0019678 propionate metabolic process, methylmalonyl pathway
Biological Process GO:1901290 succinyl-CoA biosynthetic process

Reference

[1] Chen Y, Sun W, Sun Z, Zhao H, Wu T et al.. Effect of electroacupuncture on hippocampal protein lactylation in a rat model of vascular dementia.. Front Neurol 16:1629474. 2025. PMID: 40963935.