Search Results

Overview

Uniprot IDH0VMM0
Protein NameMalonate--CoA ligase ACSF3, mitochondrial
Gene NameACSF3
OrganismCavia porcellus

Kla Sites from experimental identification

Position Flanking peptide
488 IIKTGGYKVSALEVE
568 IPRNQMGKINKKDLV

Function

Catalyzes the initial reaction in intramitochondrial fatty acid synthesis, by activating malonate and methylmalonate, but not acetate, into their respective CoA thioester. May have some preference toward very-long-chain substrates

Protein Sequence

10 MLVGAMLPRG 20 TVAFRRLACT 30 MASCRPAPRR 40 HRGHGLLHTA 50 TTARSGAAAP 60 VFTQAPGFGD 70 RVALIDQHGC 80 HTYRDLYLRS 90 LHLSQEILRL 100 RGCVDGDLQD 110 ERVSFLCSND 120 VSYVVAQWAS 130 WMSGGIAVPL 140 FPKHPPAQLE 150 YFIEDSRSSV 160 VLAGPEHVQL 170 VGPVAERLGV 180 PLLSLPPTVY 190 QGAAGEPAAV 200 APVQERKWQD 210 RGAMIIYTSG 220 TTGRPKGVLS 230 THRNLTAMVT 240 GLVHAWAWTR 250 DDVILHVLPL 260 HHMHGVVNKL 270 LCPLWVGATC 280 MMLPEFSAQQ 290 VWEKFLSLET 300 PRVNVFMAVP 310 TIYSKLLDYY 320 DQHFTQPHVR 330 DFVRAICEEK 340 IRLMVSGSAA 350 LPVPLLERWK 360 RATSHTLLER 370 YGMTEVGMAL 380 SSPLAGPRLP 390 GSVGTPLPKV 400 EVRIVSESPQ 410 RNGCPYTVHA 420 EGDAQGTKVT 430 PGLEEKEGEL 440 LVRGPSVFRE 450 YWDKPEETKC 460 AFTPDGWFRT 470 GDTAVFKDGS 480 YWIRGRTSVD 490 IIKTGGYKVS 500 ALEVERHLLA 510 HPSIADVAVI 520 GIPDMTWGQR 530 VTAVVALKAG 540 RSLSHSELKH 550 WARHFLAPYA 560 VPSELLLVEE 570 IPRNQMGKIN 580 KKDLVRQFFP 590 ESGQGPAPTM DQGPAPSG

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0090409 malonyl-CoA synthetase activity
Molecular Function GO:0031956 medium-chain fatty acid-CoA ligase activity
Molecular Function GO:0031957 very long-chain fatty acid-CoA ligase activity
Biological Process GO:0006633 fatty acid biosynthetic process
Biological Process GO:0090410 malonate catabolic process

Reference

[1] Feng J, Chen X, Li R, Xie Y, Zhang X et al.. Lactylome analysis reveals potential target modified proteins in the retina of form-deprivation myopia.. iScience 27(9):110606. 2024 Sep 20. PMID: 39246443.