Search Results

Overview

Uniprot IDO75208
Protein NameUbiquinone biosynthesis protein COQ9, mitochondrial
Gene NameCOQ9
OrganismHomo sapiens

Kla Sites from experimental identification

Position Flanking peptide
175 VQLGQAEKRKTDQFL
288 MNMGHTAKQVKSTGE

Function

Membrane-associated protein that warps the membrane surface to access and bind aromatic isoprenes with high specificity, including ubiquinone (CoQ) isoprene intermediates and presents them directly to COQ7, therefore facilitating the COQ7-mediated hydroxylase step (PubMed:25339443, PubMed:30661980, PubMed:38425362). Participates in the biosynthesis of coenzyme Q, also named ubiquinone, an essential lipid-soluble electron transporter for aerobic cellular respiration (PubMed:25339443, PubMed:30661980)

Protein Sequence

10 MAAAAVSGAL 20 GRAGWRLLQL 30 RCLPVARCRQ 40 ALVPRAFHAS 50 AVGLRSSDEQ 60 KQQPPNSFSQ 70 QHSETQGAEK 80 PDPESSHSPP 90 RYTDQGGEEE 100 EDYESEEQLQ 110 HRILTAALEF 120 VPAHGWTAEA 130 IAEGAQSLGL 140 SSAAASMFGK 150 DGSELILHFV 160 TQCNTRLTRV 170 LEEEQKLVQL 180 GQAEKRKTDQ 190 FLRDAVETRL 200 RMLIPYIEHW 210 PRALSILMLP 220 HNIPSSLSLL 230 TSMVDDMWHY 240 AGDQSTDFNW 250 YTRRAMLAAI 260 YNTTELVMMQ 270 DSSPDFEDTW 280 RFLENRVNDA 290 MNMGHTAKQV 300 KSTGEALVQG 310 LMGAAVTLKN LTGLNQRR

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005743 mitochondrial inner membrane
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0008047 enzyme activator activity
Molecular Function GO:0019840 isoprenoid binding
Molecular Function GO:0008289 lipid binding
Molecular Function GO:0042803 protein homodimerization activity
Biological Process GO:0006744 ubiquinone biosynthetic process

Reference

[1] Yang Z, Yan C, Ma J, Peng P, Ren X et al.. Lactylome analysis suggests lactylation-dependent mechanisms of metabolic adaptation in hepatocellular carcinoma.. Nat Metab 5(1):61-79. 2023 Jan. PMID: 36593272.