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Overview

Uniprot IDO75600
Protein Name2-amino-3-ketobutyrate coenzyme A ligase, mitochondrial
Gene NameGCAT
OrganismHomo sapiens

Kla Sites from experimental identification

Position Flanking peptide
193 AKLQEAQKHRLRLVA

Function

Pyridoxal phosphate (PLP) dependent enzyme, which catalyzes the cleavage of 2-amino-3-oxobutanoate to glycine and acetyl-CoA

Protein Sequence

10 MWPGNAWRAA 20 LFWVPRGRRA 30 QSALAQLRGI 40 LEGELEGIRG 50 AGTWKSERVI 60 TSRQGPHIRV 70 DGVSGGILNF 80 CANNYLGLSS 90 HPEVIQAGLQ 100 ALEEFGAGLS 110 SVRFICGTQS 120 IHKNLEAKIA 130 RFHQREDAIL 140 YPSCYDANAG 150 LFEALLTPED 160 AVLSDELNHA 170 SIIDGIRLCK 180 AHKYRYRHLD 190 MADLEAKLQE 200 AQKHRLRLVA 210 TDGAFSMDGD 220 IAPLQEICCL 230 ASRYGALVFM 240 DECHATGFLG 250 PTGRGTDELL 260 GVMDQVTIIN 270 STLGKALGGA 280 SGGYTTGPGP 290 LVSLLRQRAR 300 PYLFSNSLPP 310 AVVGCASKAL 320 DLLMGSNTIV 330 QSMAAKTQRF 340 RSKMEAAGFT 350 ISGASHPICP 360 VMLGDARLAS 370 RMADDMLKRG 380 IFVIGFSYPV 390 VPKGKARIRV 400 QISAVHSEED 410 IDRCVEAFVE VGRLHGALP

Gene Ontology

Classification GO ID Description
Biological Process GO:0006567 L-threonine catabolic process
Cellular Component GO:0005739 mitochondrion
Cellular Component GO:0016607 nuclear speck
Cellular Component GO:0005654 nucleoplasm
Cellular Component GO:0005634 nucleus
Molecular Function GO:0008890 glycine C-acetyltransferase activity
Molecular Function GO:0030170 pyridoxal phosphate binding
Biological Process GO:0006520 amino acid metabolic process

Reference

[1] Hong H, Chen X, Wang H, Gu X, Yuan Y et al.. Global profiling of protein lysine lactylation and potential target modified protein analysis in hepatocellular carcinoma.. Proteomics 23(9):e2200432. 2023 May. PMID: 36625413.