Search Results
Overview
| Uniprot ID | O94874 |
|---|---|
| Protein Name | E3 UFM1-protein ligase 1 |
| Gene Name | UFL1 |
| Organism | Homo sapiens |
Kla Sites from experimental identification
| Position | Flanking peptide |
|---|---|
| 289 | SYIKKRYKTTQLLFL |
| 351 | QVMRAFSKQASTVVF |
| 414 | LESVSTSKKDKKDER |
| 424 | KKDERRRKATEGSGS |
| 625 | ETKVALTKLHNSLNE |
Function
E3 protein ligase that mediates ufmylation, the covalent attachment of the ubiquitin-like modifier UFM1 to lysine residues on target proteins, and which plays a key role in various processes, such as ribosome recycling, response to DNA damage, interferon response or reticulophagy (also called ER-phagy) (PubMed:20018847, PubMed:20164180, PubMed:20228063, PubMed:25219498, PubMed:27351204, PubMed:30626644, PubMed:30783677, PubMed:32160526, PubMed:32807901, PubMed:35394863, PubMed:36121123, PubMed:36543799, PubMed:36893266, PubMed:37036982, PubMed:37311461, PubMed:37595036, PubMed:37795761, PubMed:38377992, PubMed:38383785, PubMed:38383789). Catalyzes ufmylation of many protein, such as CD274/PD-L1, CDK5RAP3, CYB5R3, DDRGK1, EIF6, histone H4, MRE11, P4HB, PDCD1/PD-1, TRIP4, RPN1, RPS20/uS10, RPL10/uL16, RPL26/uL24, SYVN1/HRD1 and TP53/p53 (PubMed:20018847, PubMed:20531390, PubMed:25219498, PubMed:30783677, PubMed:30886146, PubMed:32160526, PubMed:35753586, PubMed:36543799, PubMed:36893266, PubMed:37036982, PubMed:37595036, PubMed:37795761, PubMed:38383785, PubMed:38383789). As part of the UREL complex, plays a key role in ribosome recycling by catalyzing mono-ufmylation of RPL26/uL24 subunit of the 60S ribosome (PubMed:38383785, PubMed:38383789). Ufmylation of RPL26/uL24 occurs on free 60S ribosomes following ribosome dissociation: it weakens the junction between post-termination 60S subunits and SEC61 translocons, promoting release and recycling of the large ribosomal subunit from the endoplasmic reticulum membrane (PubMed:38383785, PubMed:38383789). Ufmylation of RPL26/uL24 and subsequent 60S ribosome recycling either take place after normal termination of translation or after ribosome stalling during cotranslational translocation at the endoplasmic reticulum (PubMed:37036982, PubMed:37595036, PubMed:38383785, PubMed:38383789). Involved in reticulophagy in response to endoplasmic reticulum stress by mediating ufmylation of proteins such as CYB5R3 and RPN1, thereby promoting lysosomal degradation of ufmylated proteins (PubMed:23152784, PubMed:32160526, PubMed:36543799). Ufmylation in response to endoplasmic reticulum stress is essential for processes such as hematopoiesis, blood vessel morphogenesis or inflammatory response (PubMed:32050156). Mediates ufmylation of DDRGK1 and CDK5RAP3; the role of these modifications is however unclear: as both DDRGK1 and CDK5RAP3 act as substrate adapters for ufmylation, it is uncertain whether ufmylation of these proteins is, a collateral effect or is required for ufmylation (PubMed:20018847, PubMed:20531390). Acts as a negative regulator of T-cell activation by mediating ufmylation and stabilization of PDCD1/PD-1 (PubMed:38377992). Also involved in the response to DNA damage: recruited to double-strand break sites following DNA damage and mediates monoufmylation of histone H4 and ufmylation of MRE11 (PubMed:30783677, PubMed:30886146). Mediates ufmylation of TP53/p53, promoting its stability (PubMed:32807901). Catalyzes ufmylation of TRIP4, thereby playing a role in nuclear receptor-mediated transcription (PubMed:25219498). Required for hematopoietic stem cell function and hematopoiesis (By similarity)
Protein Sequence
Gene Ontology
| Classification | GO ID | Description |
|---|---|---|
| Cellular Component | GO:0005737 | cytoplasm |
| Cellular Component | GO:0005829 | cytosol |
| Cellular Component | GO:0005783 | endoplasmic reticulum |
| Cellular Component | GO:0005789 | endoplasmic reticulum membrane |
| Cellular Component | GO:0016020 | membrane |
| Cellular Component | GO:0005741 | mitochondrial outer membrane |
| Cellular Component | GO:0043005 | neuron projection |
| Cellular Component | GO:0005634 | nucleus |
| Cellular Component | GO:0032991 | protein-containing complex |
| Cellular Component | GO:0035861 | site of double-strand break |
| Molecular Function | GO:0019901 | protein kinase binding |
| Molecular Function | GO:0061666 | UFM1 ligase activity |
| Molecular Function | GO:0071568 | UFM1 transferase activity |
| Biological Process | GO:0000077 | DNA damage checkpoint signaling |
| Biological Process | GO:0006974 | DNA damage response |
| Biological Process | GO:0006281 | DNA repair |
| Biological Process | GO:0030218 | erythrocyte differentiation |
| Biological Process | GO:0060218 | hematopoietic stem cell differentiation |
| Biological Process | GO:1903895 | negative regulation of IRE1-mediated unfolded protein response |
| Biological Process | GO:0031397 | negative regulation of protein ubiquitination |
| Biological Process | GO:0050868 | negative regulation of T cell activation |
| Biological Process | GO:0002841 | negative regulation of T cell mediated immune response to tumor cell |
| Biological Process | GO:0001649 | osteoblast differentiation |
| Biological Process | GO:0010508 | positive regulation of autophagy |
| Biological Process | GO:0008284 | positive regulation of cell population proliferation |
| Biological Process | GO:1903052 | positive regulation of proteolysis involved in protein catabolic process |
| Biological Process | GO:0140501 | positive regulation of reticulophagy |
| Biological Process | GO:1990592 | protein K69-linked ufmylation |
| Biological Process | GO:0050821 | protein stabilization |
| Biological Process | GO:0071569 | protein ufmylation |
| Biological Process | GO:0043122 | regulation of canonical NF-kappaB signal transduction |
| Biological Process | GO:0050727 | regulation of inflammatory response |
| Biological Process | GO:0033146 | regulation of intracellular estrogen receptor signaling pathway |
| Biological Process | GO:0032434 | regulation of proteasomal ubiquitin-dependent protein catabolic process |
| Biological Process | GO:0032880 | regulation of protein localization |
| Biological Process | GO:0072344 | rescue of stalled cytosolic ribosome |
| Biological Process | GO:0034976 | response to endoplasmic reticulum stress |
| Biological Process | GO:0061709 | reticulophagy |
| Biological Process | GO:0032790 | ribosome disassembly |
Reference
[1] Yang Z, Yan C, Ma J, Peng P, Ren X et al.. Lactylome analysis suggests lactylation-dependent mechanisms of metabolic adaptation in hepatocellular carcinoma.. Nat Metab 5(1):61-79. 2023 Jan. PMID: 36593272.
[2] Hong H, Chen X, Wang H, Gu X, Yuan Y et al.. Global profiling of protein lysine lactylation and potential target modified protein analysis in hepatocellular carcinoma.. Proteomics 23(9):e2200432. 2023 May. PMID: 36625413.