Search Results

Overview

Uniprot IDP00480
Protein NameOrnithine transcarbamylase, mitochondrial
Gene NameOTC
OrganismHomo sapiens

Kla Sites from experimental identification

Position Flanking peptide
144 AVLARVYKQSDLDTL
221 HLQAATPKGYEPDAS
231 EPDASVTKLAEQYAK
238 KLAEQYAKENGTKLL
289 QGYQVTMKTAKVAAS
292 QVTMKTAKVAASDWT
307 FLHCLPRKPEEVDDE
331 FPEAENRKWTIMAVM
46 GRDLLTLKNFTGEEI
70 LKFRIKQKGEYLPLL
88 SLGMIFEKRSTRTRL

Function

Catalyzes the second step of the urea cycle, the condensation of carbamoyl phosphate with L-ornithine to form L-citrulline (PubMed:2556444, PubMed:6372096, PubMed:8112735). The urea cycle ensures the detoxification of ammonia by converting it to urea for excretion (PubMed:2556444)

Protein Sequence

10 MLFNLRILLN 20 NAAFRNGHNF 30 MVRNFRCGQP 40 LQNKVQLKGR 50 DLLTLKNFTG 60 EEIKYMLWLS 70 ADLKFRIKQK 80 GEYLPLLQGK 90 SLGMIFEKRS 100 TRTRLSTETG 110 FALLGGHPCF 120 LTTQDIHLGV 130 NESLTDTARV 140 LSSMADAVLA 150 RVYKQSDLDT 160 LAKEASIPII 170 NGLSDLYHPI 180 QILADYLTLQ 190 EHYSSLKGLT 200 LSWIGDGNNI 210 LHSIMMSAAK 220 FGMHLQAATP 230 KGYEPDASVT 240 KLAEQYAKEN 250 GTKLLLTNDP 260 LEAAHGGNVL 270 ITDTWISMGQ 280 EEEKKKRLQA 290 FQGYQVTMKT 300 AKVAASDWTF 310 LHCLPRKPEE 320 VDDEVFYSPR 330 SLVFPEAENR 340 KWTIMAVMVS 350 LLTDYSPQLQ KPKF

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005743 mitochondrial inner membrane
Cellular Component GO:0005759 mitochondrial matrix
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0016597 amino acid binding
Molecular Function GO:0042802 identical protein binding
Molecular Function GO:0004585 ornithine carbamoyltransferase activity
Molecular Function GO:0042301 phosphate ion binding
Molecular Function GO:0005543 phospholipid binding
Biological Process GO:0097272 ammonium homeostasis
Biological Process GO:0019240 citrulline biosynthetic process
Biological Process GO:0042450 L-arginine biosynthetic process via ornithine
Biological Process GO:0006593 L-ornithine catabolic process
Biological Process GO:0001889 liver development
Biological Process GO:0007494 midgut development
Biological Process GO:0055081 monoatomic anion homeostasis
Biological Process GO:0070781 response to biotin
Biological Process GO:0032868 response to insulin
Biological Process GO:0009410 response to xenobiotic stimulus
Biological Process GO:0010043 response to zinc ion
Biological Process GO:0000050 urea cycle

Reference

[1] Yang Z, Yan C, Ma J, Peng P, Ren X et al.. Lactylome analysis suggests lactylation-dependent mechanisms of metabolic adaptation in hepatocellular carcinoma.. Nat Metab 5(1):61-79. 2023 Jan. PMID: 36593272.

[2] Hong H, Chen X, Wang H, Gu X, Yuan Y et al.. Global profiling of protein lysine lactylation and potential target modified protein analysis in hepatocellular carcinoma.. Proteomics 23(9):e2200432. 2023 May. PMID: 36625413.