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Overview

Uniprot IDP22315
Protein NameFerrochelatase, mitochondrial
Gene NameFech
OrganismMus musculus

Kla Sites from experimental identification

Position Flanking peptide
117 IAKRRTPKIQEQYRR
56 VHHAKTTKPQAQPER

Function

Catalyzes the ferrous insertion into protoporphyrin IX

Protein Sequence

10 MLSASANMAA 20 ALRAAGALLR 30 EPLVHGSSRA 40 CQPWRCQSGA 50 AVAATTEKVH 60 HAKTTKPQAQ 70 PERRKPKTGI 80 LMLNMGGPET 90 LGEVQDFLQR 100 LFLDRDLMTL 110 PIQNKLAPFI 120 AKRRTPKIQE 130 QYRRIGGGSP 140 IKMWTSKQGE 150 GMVKLLDELS 160 PATAPHKYYI 170 GFRYVHPLTE 180 EAIEEMERDG 190 LERAIAFTQY 200 PQYSCSTTGS 210 SLNAIYRYYN 220 EVGQKPTMKW 230 STIDRWPTHP 240 LLIQCFADHI 250 LKELNHFPEE 260 KRSEVVILFS 270 AHSLPMSVVN 280 RGDPYPQEVG 290 ATVHKVMEKL 300 GYPNPYRLVW 310 QSKVGPVPWL 320 GPQTDEAIKG 330 LCERGRKNIL 340 LVPIAFTSDH 350 IETLYELDIE 360 YSQVLAQKCG 370 AENIRRAESL 380 NGNPLFSKAL 390 ADLVHSHIQS 400 NKLCSTQLSL 410 NCPLCVNPVC 420 RKTKSFFTSQ QL

Gene Ontology

Classification GO ID Description
Cellular Component GO:0043190 ATP-binding cassette (ABC) transporter complex
Cellular Component GO:0005743 mitochondrial inner membrane
Cellular Component GO:0005759 mitochondrial matrix
Cellular Component GO:0031966 mitochondrial membrane
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0051537 2 iron, 2 sulfur cluster binding
Molecular Function GO:0004325 ferrochelatase activity
Molecular Function GO:0020037 heme binding
Molecular Function GO:0042802 identical protein binding
Molecular Function GO:0005506 iron ion binding
Molecular Function GO:0030350 iron-responsive element binding
Molecular Function GO:0042803 protein homodimerization activity
Molecular Function GO:0046906 tetrapyrrole binding
Biological Process GO:0008203 cholesterol metabolic process
Biological Process GO:0009589 detection of UV
Biological Process GO:0030218 erythrocyte differentiation
Biological Process GO:0006784 heme A biosynthetic process
Biological Process GO:0006785 heme B biosynthetic process
Biological Process GO:0006783 heme biosynthetic process
Biological Process GO:0060586 multicellular organismal-level iron ion homeostasis
Biological Process GO:0006779 porphyrin-containing compound biosynthetic process
Biological Process GO:0046501 protoporphyrinogen IX metabolic process
Biological Process GO:0010999 regulation of eIF2 alpha phosphorylation by heme
Biological Process GO:0046984 regulation of hemoglobin biosynthetic process
Biological Process GO:0009416 response to light stimulus
Biological Process GO:0034379 very-low-density lipoprotein particle assembly

Reference

[1] Zhuo W, Zhang M, Tan J, Gao Y, Wang Y et al.. Lysine lactylation analysis of proteins in the heart of the Kawasaki disease mouse model.. Front Cell Dev Biol 13:1550220. 2025. PMID: 40114965.

[2] Wu D, Tang Y, Li X, Xiong S, Zhang Z et al.. Characterization of protein lactylation in healthy and ischemic mouse hearts.. Front Cardiovasc Med 12:1644886. 2025. PMID: 41089239.