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Overview

Uniprot IDQ3UV70
Protein Name[Pyruvate dehydrogenase [acetyl-transferring]]-phosphatase 1, mitochondrial
Gene NamePdp1
OrganismMus musculus

Kla Sites from experimental identification

Position Flanking peptide
326 ERELERLKLEHPKNE

Function

Mitochondrial enzyme that catalyzes the dephosphorylation and concomitant reactivation of the alpha subunit of the E1 component of the pyruvate dehydrogenase complex (PDC), thereby stimulating the conversion of pyruvate into acetyl-CoA

Protein Sequence

10 MPAPTQLFFP 20 LVRNCELSRI 30 YGTACYCHHK 40 HLCCSPPYIP 50 QNRLRYTPHP 60 AYATFCRPRE 70 NWWQYTQGRR 80 YASTPQKFYL 90 TPPQVNSILK 100 ANEYSFKVPE 110 FDGKNVSSIL 120 GFDSNQLPAN 130 APIEDRRSAA 140 TCLQTRGMLL 150 GVFDGHAGCA 160 CSQAVSERLF 170 YYIAVSLLPH 180 ETLLEIENAV 190 ESGRALLPIL 200 QWHKHPNDYF 210 SKEASKLYFN 220 SLRTYWQELI 230 DLNTGESADI 240 DVKEALINAF 250 KRLDNDISLE 260 AQVGDPNSFL 270 NYLVLRVAFS 280 GATACVAHVD 290 GVDLHVANTG 300 DSRAMLGVQE 310 EDGSWSAVTL 320 SNDHNAQNER 330 ELERLKLEHP 340 KNEAKSVVKQ 350 DRLLGLLMPF 360 RAFGDVKFKW 370 SIDLQKRVIE 380 SGPDQLNDNE 390 YTKFIPPNYH 400 TPPYLTAEPE 410 VTYHRLRPQD 420 KFLVLATDGL 430 WETMHRQDVV 440 RIVGEYLTGM 450 HHQQPIAVGG 460 YKVTLGQMHG 470 LLTERRAKMS 480 SVFEDQNAAT 490 HLIRHAVGNN 500 EFGAVDHERL 510 SKMLSLPEEL 520 ARMYRDDITI 530 IVVQFNSHVV GAYQNQEQ

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0004741 [pyruvate dehydrogenase (acetyl-transferring)]-phosphatase activity
Molecular Function GO:0005509 calcium ion binding
Molecular Function GO:0000287 magnesium ion binding
Molecular Function GO:0004722 protein serine/threonine phosphatase activity
Molecular Function GO:0044877 protein-containing complex binding
Biological Process GO:0035970 peptidyl-threonine dephosphorylation
Biological Process GO:0140176 positive regulation of pyruvate decarboxylation to acetyl-CoA
Biological Process GO:0010510 regulation of pyruvate decarboxylation to acetyl-CoA

Reference

[1] Zhuo W, Zhang M, Tan J, Gao Y, Wang Y et al.. Lysine lactylation analysis of proteins in the heart of the Kawasaki disease mouse model.. Front Cell Dev Biol 13:1550220. 2025. PMID: 40114965.