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Overview

Uniprot IDQ64105
Protein NameSepiapterin reductase
Gene NameSpr
OrganismMus musculus

Kla Sites from experimental identification

Position Flanking peptide
215 QLARETSKDPELRSK
227 RSKLQKLKSDGALVD

Function

Catalyzes the final one or two reductions in tetra-hydrobiopterin biosynthesis to form 5,6,7,8-tetrahydrobiopterin

Protein Sequence

10 MEADGLGCAV 20 CVLTGASRGF 30 GRALAPQLAR 40 LLSPGSVMLV 50 SARSESMLRQ 60 LKEELGAQQP 70 DLKVVLAAAD 80 LGTEAGVQRL 90 LSAVRELPRP 100 EGLQRLLLIN 110 NAATLGDVSK 120 GFLNVNDLAE 130 VNNYWALNLT 140 SMLCLTSGTL 150 NAFQDSPGLS 160 KTVVNISSLC 170 ALQPYKGWGL 180 YCAGKAARDM 190 LYQVLAAEEP 200 SVRVLSYAPG 210 PLDNDMQQLA 220 RETSKDPELR 230 SKLQKLKSDG 240 ALVDCGTSAQ 250 KLLGLLQKDT 260 FQSGAHVDFY D

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005829 cytosol
Cellular Component GO:0005739 mitochondrion
Cellular Component GO:0005654 nucleoplasm
Molecular Function GO:0042803 protein homodimerization activity
Molecular Function GO:0004757 sepiapterin reductase (NADP+) activity
Biological Process GO:0048667 cell morphogenesis involved in neuron differentiation
Biological Process GO:0042417 dopamine metabolic process
Biological Process GO:0006558 L-phenylalanine metabolic process
Biological Process GO:0006809 nitric oxide biosynthetic process
Biological Process GO:0042415 norepinephrine metabolic process
Biological Process GO:0019889 pteridine metabolic process
Biological Process GO:0040014 regulation of multicellular organism growth
Biological Process GO:0042428 serotonin metabolic process
Biological Process GO:0006729 tetrahydrobiopterin biosynthetic process
Biological Process GO:0046146 tetrahydrobiopterin metabolic process
Biological Process GO:0050882 voluntary musculoskeletal movement

Reference

[1] Wu D, Tang Y, Li X, Xiong S, Zhang Z et al.. Characterization of protein lactylation in healthy and ischemic mouse hearts.. Front Cardiovasc Med 12:1644886. 2025. PMID: 41089239.