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Overview

Uniprot IDQ8BWF0
Protein NameSuccinate-semialdehyde dehydrogenase, mitochondrial
Gene NameAldh5a1
OrganismMus musculus

Kla Sites from experimental identification

Position Flanking peptide
253 PCSRNKAKEVGEVLC
353 TKFAEAMKKSLRVGN
382 KAVEKVEKQVNDAVA
399 ATVVTGGKRHQSGGN

Function

Catalyzes one step in the degradation of the inhibitory neurotransmitter gamma-aminobutyric acid (GABA)

Protein Sequence

10 MATCFLLRSF 20 WAARPALPPP 30 GRFRPEPAGT 40 PRRSYASGPG 50 GLHADLLRGD 60 SFVGGRWLPA 70 PATFPVYDPA 80 SGAKLGTVAD 90 CGVPEARAAV 100 RAAYDAFNSW 110 KGVSVKERSL 120 LLRKWYDLMI 130 QNKDDLAKII 140 TAESGKPLKE 150 AQGEILYSAL 160 FLEWFSEEAR 170 RIYGDIIYTS 180 AKDKRGLVLK 190 QPVGVAAIIT 200 PWNFPSAMIT 210 RKVGAALAAG 220 CTVVVKPAED 230 TPYSALALAQ 240 LANQAGIPAG 250 VYNVIPCSRN 260 KAKEVGEVLC 270 TDPLVSKISF 280 TGSTATGKIL 290 LHHAANSVKR 300 VSMELGGLAP 310 FIVFDSANVD 320 QAVAGAMASK 330 FRNAGQTCVC 340 SNRFLVQRGI 350 HDSFVTKFAE 360 AMKKSLRVGN 370 GFEEGTTQGP 380 LINEKAVEKV 390 EKQVNDAVAK 400 GATVVTGGKR 410 HQSGGNFFEP 420 TLLSNVTRDM 430 LCITEETFGP 440 LAPVIKFDKE 450 EEAVAIANAA 460 EVGLAGYFYS 470 QDPAQIWRVA 480 EQLEVGMVGV 490 NEGLISSVEC 500 PFGGVKQSGL 510 GREGSKYGID 520 EYLEVKYVCY GGL

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005759 mitochondrial matrix
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0031406 carboxylic acid binding
Molecular Function GO:0042802 identical protein binding
Molecular Function GO:0051287 NAD binding
Molecular Function GO:0004777 succinate-semialdehyde dehydrogenase (NAD+) activity
Biological Process GO:0007417 central nervous system development
Biological Process GO:0009450 gamma-aminobutyric acid catabolic process
Biological Process GO:0009448 gamma-aminobutyric acid metabolic process
Biological Process GO:0006536 glutamate metabolic process
Biological Process GO:0009791 post-embryonic development
Biological Process GO:0006105 succinate metabolic process

Reference

[1] Zhuo W, Zhang M, Tan J, Gao Y, Wang Y et al.. Lysine lactylation analysis of proteins in the heart of the Kawasaki disease mouse model.. Front Cell Dev Biol 13:1550220. 2025. PMID: 40114965.

[2] Wu D, Tang Y, Li X, Xiong S, Zhang Z et al.. Characterization of protein lactylation in healthy and ischemic mouse hearts.. Front Cardiovasc Med 12:1644886. 2025. PMID: 41089239.