Search Results

Overview

Uniprot IDQ91VM9
Protein NameInorganic pyrophosphatase 2, mitochondrial
Gene NamePpa2
OrganismMus musculus

Kla Sites from experimental identification

Position Flanking peptide
237 LNWFRLYKVPDGKPE
242 LYKVPDGKPENKFAF
68 IPLKADCKEEHDIPR

Function

Hydrolyzes inorganic pyrophosphate. This activity is essential for correct regulation of mitochondrial membrane potential, and mitochondrial organization and function

Protein Sequence

10 MRALLPLLSV 20 GRGWRVGAAA 30 RPPRRVMSLY 40 RTEELGHPRS 50 QDYRLFFKHV 60 AGHYISPFHD 70 IPLKADCKEE 80 HDIPRKKARN 90 DEYENLFNMV 100 VEIPRWTNAK 110 MEIATEEPLN 120 PIKQDIKNGK 130 LRYTPNIFPH 140 KGYIWNYGAL 150 PQTWEDPHLR 160 DKSTDCCGDN 170 DPIDVCEIGS 180 KVLSRGDVVH 190 VKILGTLALI 200 DQSETDWKII 210 AINVNDPEAE 220 KFHDIDDVKK 230 FKPGYLEATL 240 NWFRLYKVPD 250 GKPENKFAFN 260 GEFKNKAFAL 270 DVINSAHERW 280 KEMVMKKCDK 290 GAISCVNVHI 300 CDSPFHCTME 310 EARSLVESVP 320 TPSMNKESNV 330 EEEVWHFLRN

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005739 mitochondrion
Cellular Component GO:0045202 synapse
Molecular Function GO:0004427 inorganic diphosphate phosphatase activity
Molecular Function GO:0000287 magnesium ion binding
Molecular Function GO:0004722 protein serine/threonine phosphatase activity
Biological Process GO:0071344 diphosphate metabolic process
Biological Process GO:0006796 phosphate-containing compound metabolic process
Biological Process GO:0051881 regulation of mitochondrial membrane potential

Reference

[1] Zhuo W, Zhang M, Tan J, Gao Y, Wang Y et al.. Lysine lactylation analysis of proteins in the heart of the Kawasaki disease mouse model.. Front Cell Dev Biol 13:1550220. 2025. PMID: 40114965.

[2] Wu D, Tang Y, Li X, Xiong S, Zhang Z et al.. Characterization of protein lactylation in healthy and ischemic mouse hearts.. Front Cardiovasc Med 12:1644886. 2025. PMID: 41089239.