Search Results

Overview

Uniprot IDQ99JT1
Protein NameGlutamyl-tRNA(Gln) amidotransferase subunit B, mitochondrial
Gene NameGatb
OrganismMus musculus

Kla Sites from experimental identification

Position Flanking peptide
529 RNPKAINKLIGLVRK

Function

Allows the formation of correctly charged Gln-tRNA(Gln) through the transamidation of misacylated Glu-tRNA(Gln) in the mitochondria. The reaction takes place in the presence of glutamine and ATP through an activated gamma-phospho-Glu-tRNA(Gln)

Protein Sequence

10 MAAPMLRLGF 20 PGRRWALTWL 30 DGGSRHRSGS 40 QTGPTSNWAR 50 RQSSVAQPSL 60 HTAQKPRKGE 70 HKWAAVVGLE 80 IHAQISSNSK 90 LFSGAQVCFA 100 APPNSLVSYF 110 DASLPGTLPV 120 LNRRCVEAAV 130 MTGLALNCHI 140 NKKSLFDRKH 150 YFYSDLPAGY 160 QITQQRLPIA 170 ANGHLTYCIY 180 LGKKPSQVTT 190 KTVRIKQIQL 200 EQDSGKSLHD 210 DLRSQTLIDL 220 NRAGIGLLEV 230 VLEPDLCCGE 240 EAALAVRELQ 250 LILQALGTSQ 260 ANMAEGQLRV 270 DANISVHHPG 280 EPLGVRTEVK 290 NLNSLRFLAK 300 AIDYEIQRQI 310 TELENGGEIL 320 NETRSFDYKL 330 GCTMPMRDKE 340 GKQDYRFMPE 350 PNLPPLVLYD 360 DTSLPRGADS 370 QQVINIDQLR 380 DMLPELPSAT 390 RERLVQQYGM 400 LPEHSFALLN 410 EVGLLEFFQN 420 VIKETRTEPK 430 KVTNWVLNTF 440 LCYLKQQNLA 450 VSESPVTPSA 460 LAELLNLLDR 470 KAISSSAAKQ 480 VFEELWKGEG 490 KTAAQIVSEQ 500 QLELMQDQEA 510 LEKLCQTTID 520 GHPQVVMDVK 530 KRNPKAINKL 540 IGLVRKASHS 550 RADPALIKKI LERKLSL

Gene Ontology

Classification GO ID Description
Cellular Component GO:0030956 glutamyl-tRNA(Gln) amidotransferase complex
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0005524 ATP binding
Molecular Function GO:0050567 glutaminyl-tRNA synthase (glutamine-hydrolyzing) activity
Biological Process GO:0070681 glutaminyl-tRNAGln biosynthesis via transamidation
Biological Process GO:0032543 mitochondrial translation

Reference

[1] Zhuo W, Zhang M, Tan J, Gao Y, Wang Y et al.. Lysine lactylation analysis of proteins in the heart of the Kawasaki disease mouse model.. Front Cell Dev Biol 13:1550220. 2025. PMID: 40114965.