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Overview

Uniprot IDQ99KB8
Protein NameHydroxyacylglutathione hydrolase, mitochondrial
Gene NameHagh
OrganismMus musculus

Kla Sites from experimental identification

Position Flanking peptide
114 DHAGGNEKLVKLEPG
117 GGNEKLVKLEPGLKV

Function

Thiolesterase that catalyzes the hydrolysis of S-D-lactoyl-glutathione to form glutathione and D-lactic acid

Protein Sequence

10 MVLGRGSLCL 20 RSLSALGATC 30 ARRGLGQALL 40 GLSLCHSDFR 50 KNLTVQQDIM 60 KVELLPALTD 70 NYMYLIIDED 80 TQEAAIVDPV 90 QPQKVIEAAK 100 KHHVKLTTVL 110 TTHHHWDHAG 120 GNEKLVKLEP 130 GLKVYGGDDR 140 IGALTHKVTH 150 LSTLQVGSLS 160 VKCLSTPCHT 170 SGHICYFVSK 180 PGSSEPSAVF 190 TGDTLFVAGC 200 GKFYEGTADE 210 MYKALLEVLG 220 RLPPDTKVYC 230 GHEYTVNNLK 240 FARHVEPGNA 250 AIQEKLAWAK 260 EKYAIGEPTV 270 PSTLAEEFTY 280 NPFMRVKEKT 290 VQQHAGETDP 300 VTTMRAIRRE KDQFKVPRD

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005737 cytoplasm
Cellular Component GO:0005759 mitochondrial matrix
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0004416 hydroxyacylglutathione hydrolase activity
Molecular Function GO:0046872 metal ion binding
Biological Process GO:0006750 glutathione biosynthetic process
Biological Process GO:0006749 glutathione metabolic process
Biological Process GO:0019243 methylglyoxal catabolic process to D-lactate via S-lactoyl-glutathione

Reference

[1] Zhuo W, Zhang M, Tan J, Gao Y, Wang Y et al.. Lysine lactylation analysis of proteins in the heart of the Kawasaki disease mouse model.. Front Cell Dev Biol 13:1550220. 2025. PMID: 40114965.

[2] Wu D, Tang Y, Li X, Xiong S, Zhang Z et al.. Characterization of protein lactylation in healthy and ischemic mouse hearts.. Front Cardiovasc Med 12:1644886. 2025. PMID: 41089239.