Search Results

Overview

Uniprot IDQ99L13
Protein Name3-hydroxyisobutyrate dehydrogenase, mitochondrial
Gene NameHibadh
OrganismMus musculus

Kla Sites from experimental identification

Position Flanking peptide
124 GILKKVKKGSLLIDS
78 PDVCKEFKEAGEQVA

Function

No function data available.

Protein Sequence

10 MAASLGFRGA 20 ASGLWYWSGR 30 RRPVGSLAAV 40 CSRSMASKTP 50 VGFIGLGNMG 60 NPMAKNLMKH 70 GYPLILYDVF 80 PDVCKEFKEA 90 GEQVASSPAE 100 VAEKADRIIT 110 MLPSSMNAVE 120 VYSGANGILK 130 KVKKGSLLID 140 SSTIDPSVSK 150 ELAKEVEKMG 160 AVFMDAPVSG 170 GVGAARSGNL 180 TFMVGGVEDE 190 FAAAQELLEC 200 MGSNVVYCGA 210 VGTGQSAKIC 220 NNMLLAISMI 230 GTAEAMNLGI 240 RSGLDPKLLA 250 KILNMSSGRC 260 WSSDTYNPVP 270 GVMHGVPSSN 280 NYQGGFGTTL 290 MAKDLGLAQD 300 SATSTKTPIL 310 LGSLAHQIYR 320 MMCSKGYSKK 330 DFSSVFQYLR EEEPF

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005739 mitochondrion
Molecular Function GO:0008442 3-hydroxyisobutyrate dehydrogenase activity
Molecular Function GO:0051287 NAD binding
Molecular Function GO:0050661 NADP binding
Biological Process GO:0006574 L-valine catabolic process

Reference

[1] Chang J, Wu W, Qian P, Lu Z, He X et al.. Multi-omics study on the effect of moderate-intensity exercise on protein lactylation in mouse muscle tissue.. Front Cell Dev Biol 12:1472338. 2024. PMID: 39935788.

[2] Zhuo W, Zhang M, Tan J, Gao Y, Wang Y et al.. Lysine lactylation analysis of proteins in the heart of the Kawasaki disease mouse model.. Front Cell Dev Biol 13:1550220. 2025. PMID: 40114965.

[3] Wu D, Tang Y, Li X, Xiong S, Zhang Z et al.. Characterization of protein lactylation in healthy and ischemic mouse hearts.. Front Cardiovasc Med 12:1644886. 2025. PMID: 41089239.