Search Results
Overview
| Uniprot ID | Q9D7B6 |
|---|---|
| Protein Name | Isobutyryl-CoA dehydrogenase, mitochondrial |
| Gene Name | Acad8 |
| Organism | Mus musculus |
Kla Sites from experimental identification
| Position | Flanking peptide |
|---|---|
| 229 | TPGLSFGKKEKKVGW |
| 78 | FPVDVMRKAAQLGFG |
Function
Isobutyryl-CoA dehydrogenase which catalyzes the conversion of 2-methylpropanoyl-CoA to (2E)-2-methylpropenoyl-CoA in the valine catabolic pathway. To a lesser extent, also able to catalyze the oxidation of (2S)-2-methylbutanoyl-CoA
Protein Sequence
10
MAMLRSGYRR
20
FGCLRAALKS
30
LAQTHHRSIT
40
FCIDPSLGLN
50
EEQKGFQKVA
60
FDFAAREMAP
70
NMAEWDQKEL
80
FPVDVMRKAA
90
QLGFGGVYVR
100
TDVGGSGLSR
110
LDTSVIFEAL
120
ATGCTSTTAY
130
ISIHNMCAWM
140
IDSFGNEEQR
150
HKFCPPLCTM
160
EKFASYCLTE
170
PGSGSDAASL
180
LTSAKQQGDH
190
YILNGSKAFI
200
SGGGESDIYV
210
VMCRTGGSGA
220
KGISCIVVEK
230
GTPGLSFGKK
240
EKKVGWNSQP
250
TRAVIFEDCA
260
VPVANRIGTE
270
GQGFLIAMKG
280
LNGGRINVAS
290
CSLGAAHASV
300
ILTQEHLKVR
310
KQFGAPLARS
320
QYLQFQLADM
330
ATKLVASRLM
340
IRTAAVALQE
350
EREDAVALCS
360
MAKLFATEEC
370
FAICNQALQM
380
HGGYGYLKDY
390
AVQQYMRDSR
400
VHQILEGSNE
410
VMRMLISRNL
LQD
Gene Ontology
| Classification | GO ID | Description |
|---|---|---|
| Cellular Component | GO:0005739 | mitochondrion |
| Molecular Function | GO:0050660 | flavin adenine dinucleotide binding |
| Molecular Function | GO:0003853 | short-chain 2-methyl fatty acyl-CoA dehydrogenase activity |
| Biological Process | GO:0006635 | fatty acid beta-oxidation |
| Biological Process | GO:0006574 | L-valine catabolic process |
Reference
[1] Zhuo W, Zhang M, Tan J, Gao Y, Wang Y et al.. Lysine lactylation analysis of proteins in the heart of the Kawasaki disease mouse model.. Front Cell Dev Biol 13:1550220. 2025. PMID: 40114965.