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Overview

Uniprot IDQ9H2Y7
Protein NameZinc finger protein 106
Gene NameZNF106
OrganismHomo sapiens

Kla Sites from experimental identification

Position Flanking peptide
557 NPLLSTSKSTRNYAK

Function

RNA-binding protein. Specifically binds to 5'-GGGGCC-3' sequence repeats in RNA. Essential for maintenance of peripheral motor neuron and skeletal muscle function. Required for normal expression and/or alternative splicing of a number of genes in spinal cord and skeletal muscle, including the neurite outgrowth inhibitor RTN4. Also contributes to normal mitochondrial respiratory function in motor neurons, via an unknown mechanism

Protein Sequence

10 MPVGRIECPS 20 SPSFPRDISH 30 ECRVCGVTEV 40 GLSAYAKHIS 50 GQLHKDNVDA 60 QEREDDGKGE 70 EEEEDYFDKE 80 LIQLIKQRKE 90 QSRQDEPSNS 100 NQEINSDDRR 110 PQWRREDRIP 120 YQDRESYSQP 130 AWHHRGPPQR 140 DWKWEKDGFN 150 NTRKNSFPHS 160 LRNGGGPRGR 170 SGWHKGVAGG 180 SSTWFHNHSN 190 SGGGWLSNSG 200 AVDWNHNGTG 210 RNSSWLSEGT 220 GGFSSWHMNN 230 SNGNWKSSVR 240 STNNWNYSGP 250 GDKFQPGRNR 260 NSNCQMEDMT 270 MLWNKKSNKS 280 NKYSHDRYNW 290 QRQENDKLGT 300 VATYRGPSEG 310 FTSDKFPSEG 320 LLDFNFEQLE 330 SQTTKQADTA 340 TSKVSGKNGS 350 AAREKPRRWT 360 PYPSQKTLDL 370 QSGLKDITGN 380 KSEMIEKPLF 390 DFSLITTGIQ 400 EPQTDETRNS 410 PTQKTQKEIH 420 TGSLNHKASS 430 DSAASFEVVR 440 QCPTAEKPEQ 450 EHTPNKMPSL 460 KSPLLPCPAT 470 KSLSQKQDPK 480 NISKNTKTNF 490 FSPGEHSNPS 500 NKPTVEDNHG 510 PYISKLRSSC 520 PHVLKGNKST 530 FGSQKQSGDN 540 LNDTLRKAKE 550 VLQCHESLQN 560 PLLSTSKSTR 570 NYAKASRNVE 580 ESEKGSLKIE 590 FQVHALEDES 600 DGETSDTEKH 610 GTKIGTLGSA 620 TTELLSGSTR 630 TADEKEEDDR 640 ILKTSRELST 650 SPCNPIVRQK 660 ESELQMTSAA 670 SPHPGLLLDL 680 KTSLEDAQVD 690 DSIKSHVSYE 700 TEGFESASLD 710 AELQKSDISQ 720 PSGPLLPELS 730 KLGFPASLQR 740 DLTRHISLKS 750 KTGVHLPEPN 760 LNSARRIRNI 770 SGHRKSETEK 780 ESGLKPTLRQ 790 ILNASRRNVN 800 WEQVIQQVTK 810 KKQELGKGLP 820 RFGIEMVPLV 830 QNEQEALDLD 840 GEPDLSSLEG 850 FQWEGVSISS 860 SPGLARKRSL 870 SESSVIMDRA 880 PSVYSFFSEE 890 GTGKENEPQQ 900 MVSPSNSLRA 910 GQSQKATMHL 920 KQEVTPRAAS 930 LRTGERAENV 940 ATQRRHSAQL 950 SSDHIIPLMH 960 LAKDLNSQER 970 SIPPSENQNS 980 QESNGEGNCL 990 SSSASSALAI 1000 SSLADAATDS 1010 SCTSGAEQND 1020 GQSIRKKRRA 1030 TGDGSSPELP 1040 SLERKNKRRK 1050 IKGKKERSQV 1060 DQLLNISLRE 1070 EELSKSLQCM 1080 DNNLLQARAA 1090 LQTAYVEVQR 1100 LLMLKQQITM 1110 EMSALRTHRI 1120 QILQGLQETY 1130 EPSEHPDQVP 1140 CSLTRERRNS 1150 RSQTSIDAAL 1160 LPTPFFPLFL 1170 EPPSSHVSPS 1180 PTGASLQITT 1190 SPTFQTHGSV 1200 PAPDSSVQIK 1210 QEPMSPEQDE 1220 NVNAVPPSSA 1230 CNVSKELLEA 1240 NREISDSCPV 1250 YPVITARLSL 1260 PESTESFHEP 1270 SQELKFSVEQ 1280 RNTRNRENSP 1290 SSQSAGLSSI 1300 NKEGEEPTKG 1310 NSGSEACTSS 1320 FLRLSFASET 1330 PLEKEPHSPA 1340 DQPEQQAEST 1350 LTSAETRGSK 1360 KKKKLRKKKS 1370 LRAAHVPENS 1380 DTEQDVLTVK 1390 PVRKVKAGKL 1400 IKGGKVTTST 1410 WEDSRTGREQ 1420 ESVRDEPDSD 1430 SSLEVLEIPN 1440 PQLEVVAIDS 1450 SESGEEKPDS 1460 PSKKDIWNST 1470 EQNPLETSRS 1480 GCDEVSSTSE 1490 IGTRYKDGIP 1500 VSVAETQTVI 1510 SSIKGSKNSS 1520 EISSEPGDDD 1530 EPTEGSFEGH 1540 QAAVNAIQIF 1550 GNLLYTCSAD 1560 KTVRVYNLVS 1570 RKCIGVFEGH 1580 TSKVNCLLVT 1590 QTSGKNAALY 1600 TGSSDHTIRC 1610 YNVKSRECVE 1620 QLQLEDRVLC 1630 LHSRWRILYA 1640 GLANGTVVTF 1650 NIKNNKRLEI 1660 FECHGPRAVS 1670 CLATAQEGAR 1680 KLLVVGSYDC 1690 TISVRDARNG 1700 LLLRTLEGHS 1710 KTILCMKVVN 1720 DLVFSGSSDQ 1730 SVHAHNIHTG 1740 ELVRIYKGHN 1750 HAVTVVNILG 1760 KVMVTACLDK 1770 FVRVYELQSH 1780 DRLQVYGGHK 1790 DMIMCMTIHK 1800 SMIYTGCYDG 1810 SIQAVRLNLM 1820 QNYRCWWHGC 1830 SLIFGVVDHL 1840 KQHLLTDHTN 1850 PNFQTLKCRW 1860 KNCDAFFTAR 1870 KGSKQDAAGH 1880 IERHAEDDSK IDS

Gene Ontology

Classification GO ID Description
Cellular Component GO:0005829 cytosol
Cellular Component GO:0016020 membrane
Cellular Component GO:0016607 nuclear speck
Cellular Component GO:0005730 nucleolus
Molecular Function GO:0003723 RNA binding
Molecular Function GO:0008270 zinc ion binding
Biological Process GO:0008286 insulin receptor signaling pathway

Reference

PMID: N/A